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VON HIPPEL-LINDAU TUMOR SUPPRESSOR PROTEIN
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DeCS
Descriptor
English
:
Von Hippel-Lindau Tumor Suppressor Protein
Descriptor
Spanish
:
Proteína Supresora de Tumores del Síndrome de Von Hippel-Lindau
Descriptor
Portuguese
:
Proteína Supressora de Tumor Von Hippel-Lindau
Tree Number:
D08.811.464.938.750.875
D12.776.624.776.865
Definition
English
:
A ubiquitin-protein ligase that mediates OXYGEN-dependent polyubiquitination of
HYPOXIA-INDUCIBLE FACTOR 1
, ALPHA SUBUNIT. It is inactivated in VON HIPPEL-LINDAU
SYNDROME.
Entry Combination - descr/qualif
English
:
Von Hippel-Lindau Tumor Suppressor Protein
/
deficiency
use
von Hippel-Lindau Disease
History Note
English
:
2006(1995)
Allowable Qualifiers
English
:
administration & dosage
adverse effects
antagonists & inhibitors
analysis
biosynthesis
blood
cerebrospinal fluid
chemistry
classification
chemical synthesis
contraindications
drug effects
diagnostic use
economics
genetics
history
immunology
isolation & purification
metabolism
pharmacology
physiology
pharmacokinetics
poisoning
radiation effects
supply & distribution
secretion
standards
toxicity
therapeutic use
ultrastructure
urine
Record Number:
50588
Unique Identifier:
D051794
Occurrence in VHL
:
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